ADAMTS13

Abbreviation:ADAMTS13
Aliases:ADAM metallopeptidase with thrombospondin type 1 motif, 13, VWFCP
Gene Symbol:ADAMTS13 
SubUnit:
Type:metalloprotease
Main Action:vWF-cleaving protease
Genomic Reference Sequence:NG_011934.2
Locus Reference Genomic (LRG):LRG_544
LOVD:https://www.LOVD.nl/ADAMTS13
Locus Specific Database (LSDB):
Amino Acid Numbering Conversion Factor (Old > New;+/-):
Variant Details: ADAMTS13 (1)
Predicted Mr (da):153,604
Predicted pl:7
Gene Size (bp):37,404
Transcript Size (nt):4,951
Number of Exons:29
Gene Location:9q34
Number of Amino Acids:1,427
Mature Protein:75-1427
Observer Mr of Monomer (kDa):
Plasma Concentration (ug/ml):1000
Plasma Molarity (nM):5
Half-life (h):48-72
cDNA Reference Sequence (NM):NM_139025.4
Protein Reference Sequence (NP):NP_620594.1
Reference cDNA Sequence +1ATG (fasta format):https://coagbase.org/wp-content/uploads/2022/01/NM_139025.fasta
Reference cDNA Sequence +1ATG (GenBank format):https://coagbase.org/wp-content/uploads/2022/01/NM_139025.gb
Reference cDNA Sequence +1ATG with translation and exons marked (pdf format):https://coagbase.org/wp-content/uploads/2022/01/NM_139025_ADAMTS13.pdf